[CIS PIDD] Post-Fontan hypogam

[Boyce, Thomas G., M.D.]

Agree usually albumin is low in PLE but would check a stool alpha 1 antitrypsin to see if losing protein in stool. Also very hard to replete IgG in pts with PLE. 



On Aug 21, 2012, at 8:29 PM, "Church, Joseph" <JChurch at chla.usc.edu> wrote:


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> Colleagues:

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> I follow an 8yo boy with the following

>             - Protein losing enteropathy (history of)

>             - Fontan procedure for hypoplastic left heart

>             - IgG 334 IgA 50 IgM58

>             - CD3+ 26% (308), CD19 42% (478)

>             - Serum albumin 4.7 mg/dL.

>  

> Has any one seen this pattern of immunodeficiency in the face of a very normal serum albumin level?

>  

> Thank you for your thoughts.

>  

> Joe Church

> Children's Hospital Los Angeles

> 

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