[CIS-PAGID] deficiency in terminal complement components

[Saxon, Andy M.D.]

We have always treated (the few adults we have seen) with vaccination and prophylaxis as their sepsis/meningitis can be so rapid as to be untreatable once they even get non-specific symptoms. Plus it puts an extra burden on the patient to know when to take the medicine rather than taking it daily.

The patients who get recognized in new families are lucky to be alive...

A. Saxon, MD
UCLA

-----Original Message-----
From: pagid-bounces at list.clinimmsoc.org [mailto:pagid-bounces at list.clinimmsoc.org] On Behalf Of Philipp Henneke
Sent: Thursday, December 01, 2011 3:09 AM
To: pagid at list.clinimmsoc.org
Subject: [CIS-PAGID] deficiency in terminal complement components

We have recently diagnosed a patient with recurrent meningococcal meningitis to be deficient in terminal complement components.
My question: What is the experience with antibiotic prophylaxis versus preemptive treatment when non specific symptoms of infection occur?
Philipp Henneke

Prof. Dr. med. Philipp Henneke

UNIVERSITÄTSKLINIKUM FREIBURG
Centrum für Chronische Immundefizienz (CCI) Zentrum für Kinder- und Jugendmedizin

Tel Sekretariat 0761 270-77640
Tel mobil 0162 285 2481
Fax 0761 270 77600
Breisacherstr. 117-2.OG, 79106 Freiburg
philipp.henneke at uniklinik-freiburg.de
http://www.cci.uniklinik-freiburg.de




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