[CIS PIDD] [cis-pidd] CVID, NRH and HSCT?

[Zachary D. Jacobs, MD]

Hello all,

I follow 40 year-old man with CVID, diagnosed about 15 years ago.  For the
last several years he has had worsening nodular regenerative hyperplasia
associated with his disease, eventually causing portal hypertension,
hepatic encephalopathy and TIPS placement.  He is now on the liver
transplant list and has actually been given a waiver for this, given his
CVID.  Hepatology would like for him to receive a HSCT within 90 days of
him receiving his new liver (assuming the transplant happens), to minimize
the risk of the pathophysiology repeating itself.

Does anyone have any experience with this?  Would an immunology center in
the US like to evaluate him any further for this?

Thanks,

Zach

-- 
Zachary D. Jacobs, M.D.

The Center for Allergy & Immunology

Saint Luke’s Physician Partners
Medical Plaza II
4330 Wornall, Suite 40
Kansas City, MO 64111

Ph: 816.531.0930
Fax: 816.753.2671

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