[CIS PIDD] [cis-pidd] lung transplant in CVID patients with GLID?

[Routes, John]

HI Elena
I am not aware of any studies on this, although my guess is there are
isolated case reports‹there are reports on lung transplantion in CVID and
bronchiectasis with or without hypogammaglobulinemia‹
you didnt mention how many courses of RTX the patient got and how long Rx
with immuran‹‹we have retreated some or our patients
also, might want to consider pulse methylprednisolone and see if she has
any reversible component
good luck
Jack
 
John M. Routes, MD
Chief, Section of Allergy and Clinical Immunology
Professor of Pediatrics, Medicine, Microbiology and Molecular Genetics
Department of Pediatrics
Children's Hospital of Wisconsin
Medical College of Wisconsin
9000 W. Wisconsin Ave.
Milwaukee, WI  53226-4874
Phone: Office 414-266-6840
Fax: 414-266-6437
Email: jroutes at mcw.edu




On 7/16/15, 12:02 AM, "Elena Hsieh" <whsieh at stanford.edu> wrote:

>Hi there,
>
>We have a very sick 48yo woman with CVID and granulomatous-lymphocytic
>interstitial lung disease (GLILD), who has now developed pulmonary
>hypertension, s/p rituximab and imuran, currently not doing well.  Is
>there a precedent for lung transplant in CVID patients with GLILD who
>fail improvement with immunosuppressive regimen? If so, could you point
>me to a good reference?
>
>Thanks.
>Elena
>
>Instructor
>Allergy and Immunology
>Stanford University
>
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