[CIS PIDD] [cis-pidd] Raynaud's in XLA

[CIS-PIDD]

Mikko,
Thank you. No other symptoms. Studies are pending. If anything turns up,
I'll post it.
Richard


On Wed, Jan 3, 2018 at 12:26 AM, CIS-PIDD <cis-pidd at lists.clinimmsoc.org>
wrote:

> Hi Richard,
>
>
>
> have you checked for LGL leukemia? Gulbu, Kate (CHOP) and Steve & various
> other colleagues in NIH have described a series of XLA patients with LGL-L/
> LGL lymphoproliferation in XLA during follow up (I think still only as a
> poster). Appears around that age…
>
>
>
> No other suggestive autoimmune features? Cytopenias (RBC/PLT/PMN/Ly)?
> Blood smear/ T cell clonality?
>
>
>
> Mikko
>
>
>
>
>
>
>
> *Mikko Seppänen*
>
> Director, Adjunct Professor, MD, PhD
>
> *Hospital District of Helsinki and Uusimaa, Children’s Hospital, Rare
> Disease Center *
>
> P.O.Box 280, 00029 HUS |Lastenlinnantie 2, Helsinki
> <https://maps.google.com/?q=Lastenlinnantie+2,+Helsinki&entry=gmail&source=g>
>
> Senior Consultant
>
> *Hospital District of Helsinki and Uusimaa, Inflammation Center, Adult
> Primary Immunodeficiency Outpatient Clinic *
> mikko.seppanen at hus.fi
>
> +358 9 47180201[image:
> http://helmeias141v.hus.fi/sinfoweb/images/PointY.gif]| +358 50 4279606
> <+358%2050%204279606>
> faxi +358 9 47174703 <+358%209%2047174703>
>
> www.hus.fi; www.harvinaissairaudet.fi
>
>  [image: cid:image002.jpg at 01D21E2C.7B3D60A0]
>
>
>
>
>
>
>
>
>
> *Lähettäjä:* cis-pidd at lyris.dundee.net [mailto:cis-pidd at lyris.dundee.net] *Puolesta
> *CIS-PIDD
> *Lähetetty:* 2. tammikuuta 2018 23:02
> *Vastaanottaja:* CIS-PIDD <cis-pidd at lyris.dundee.net>
> *Aihe:* [cis-pidd] Raynaud's in XLA
>
>
>
> I have followed a 39 yo XLA for 34 years. Other than sinusitis twice a
> year he has had no problems. He now has Raynaud's of the hands for the past
> 2-3 years that is worsening.
>
>
>
> Is the generally recommended treatment, calcium channel blocker, ideal in
> this setting?
>
> Thanks,
>
> Richard
>
>
>
> --
>
> Richard L. Wasserman, MD, PhD
> Allergy Partners of North Texas
> 7777 Forest Lane, Suite B
> <https://maps.google.com/?q=7777+Forest+Lane,+Suite+B&entry=gmail&source=g>
> -332
> Dallas, Texas 75230
> Office (972) 566-7788
> Fax (972) 566-8837
> Cell (214) 697-7211
>
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-- 
Richard L. Wasserman, MD, PhD
Allergy Partners of North Texas
7777 Forest Lane, Suite B-332
Dallas, Texas 75230
Office (972) 566-7788
Fax (972) 566-8837
Cell (214) 697-7211

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