[PAGID] progressive loss of hearing in 6 year old boy

[C. Lucy Park]

Try to contact Dr. Yoo at Univesity of Tennessee. His research is on
autoimmune hearing loss.
tyoo at utmem.edu
http://www.utmem.edu/neuroscience/faculty/T_Yoo.php



On Thu, Sep 10, 2009 at 8:11 AM, Walther, Joachim-Ulrich Prof.Dr. <
Ju.Walther at med.uni-muenchen.de> wrote:


>  To whom it may concern

>

> Dear colleagues,

>

> in the hope to direct my inquiry properly and adequately I put the

> following question to clinicians and immunologists involved in acquired

> deafness.

> I shall be extremely grateful for your comments and advice

>

> *Case:*

> Six year old boy, otherwise apart from mild gross motor retardation

> healthy.

> Left ear found to be nearly completely deaf at five years, apparently after

> an underestimated loss of function over the years. Neonatal hearing test

> normal.

> Now quickly developing (within a few months) loss of hearing

> contralaterally (low frequency spectrum). One course of steroid and osmotoc

> iv therapy given. During the few weeks since no improvement and no

> progression.    No family history, no consanguinity.

> Clinically unremarkable.

> No signs of inflammation and autoimmune activation in laboratory results.

> Ophthalmological findings normal.

> Audiologist´s interpretation:    autoimmune mediated loss of hearing.

> Advice: immunosuppressive therapy.

> Our question: is this indicated ?

> Genetic diagnosis is being considered, particularly to be able to avoid

> unnnecessary immunosuppression.

>

> Many thanks for your help

>

>   *Prof.Dr.med.J.-U.Walther M.Sc.*

> *Allgemeinpädiatrischen Ambulanz *

> *der Kinderklinik und Kinderpoliklinik*

> *im Dr.v.Haunerschen Kinderspital*

> *der Ludwig-Maximilians-Universität*

> *Lindwurmstraße 4*

> *80337  München*

> **

> *Tel.:    089 / 5160-2811*

> *Fax:      "        "   -7722*

> *mail:    **Ju.Walther at med.uni-muenchen.de*

>

>




-- 
C. Lucy Park, MD
Head, Division of Allergy-Immunology-Pulmonology
Dpt of Pediatrics
University of Illinois at Chicago
840 S. Wood St., Suite1306
Chicago, IL 60612
Tel: 312-996-6714
Fax: 312-413-8694
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