[CIS PIDD] [cis-pidd] Fwd: Hyper IgE syndrome

[Fabrício Prado Monteiro]

Luciana, afastou S. de Wiskot-Audrich?
Dose alfa-feto-ptn e a deficiência da WASP, em Curitiba ok?

                                   F!
www.imunoped.com.br







Il giorno 28/mar/2013, alle ore 20:45, luciana Cunha <lucianaaoc at gmail.com> ha scritto:


> 

> Dear friends:

> 

> I would like to discuss a case.

> We admitted at ICU a 7 year-old girl who was being treated as a severe atopic dermatitis, presenting with a staphylococcal and pseudomonas sepsis. She also has eosinophilia (>2000/mL), normal immunoglobulins levels, normal lymphocyte immunophenotyping ( CD3,CD4, CD8 CD19, CD16/56), primary teeth retention, chronic eczema, characteristic face and high palate. She doesn't present pneumonias or parenchimal lung anomalies. She is from a consanguinous family with many cases of less severe atopic dermatitis. 

> At the moment, she is using vancomycin, cefepime, prednisone 1mg/kg/day and diphenydramine. We are considering the use of gammaglobulin or omalyzumab. What's your opinion? Any other suggestion? 

> Thank you very much,

>  

> Luciana Cunha

> Primary Immunodeficiency Service

> Federal University of Minas Gerais

> Brazil

> 

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